The genetic defect is so named after its tell-tale symptom of characteristic, sweet smeling body secretions like urine, sweat, and earwax that is oddly reminiscent of maple syrup. Itâs more likely that youâll notice this smell once your baby is a little older (6 months-1.5 years) and it could either be the urine or his sweat that smells like maple syrup. There was one assessor who described one of the fenugreek odor compounds as â[m]usty, sweet, onion, socks.â Another agreed, but thought it more like â[f]ruity, floral, socks.â Of course, there was the boring assessor who was like, uh, smells like fenugreek. Rocky, do a search on â¦ The bedroom, the closet and the bathroom, so itâs something in that area. I have never heard of someones sweat smelling like maple syrup. In the past, doctors followed their noses toward the source of many diseases. It doesn't even smell like sweat. Function . Some medical conditions (or eating fenugreek in high quantities) can cause urine/sweat to smell like syrup. I'd air out the room too, and see if you can't literally pinpoint the smell by finding where in the room it smells like it's coming from. They eventually spill over into the urine, giving it a maple syrup-like smell. There's a maple syrup urine disease in people which I've never diagnosed in dogs most likely because it's caused by the excessive intake of branched-chain amino acids which smell like maple syrup. Sweet-smelling urine may be caused by diet, diabetes, or maple syrup urine disease. It is likely the result of mild dehydration overnight, especially if your baby doesnât wake for feedings overnight, or sweat buildup due to wearing warm clothes. Stop all forms of sugar and alcohol and obtain high dose thiamine from the health food store. For some reason, some children will periodically have a maple syrup smell in their sweat. Sluggish/slow/tiredness and weakness. I sometimes catch of whiff of that smell from my daughter, although we â¦ » Review Causes of Maple syrup urine odor in children: Causes Together with sweet urine, it is accompanied with several neurological symptoms. Some people describe it as smelling somewhat like maple syrup while others associate it more closely with butterscotch. Tampa_Terry. But I love maple more than chocolate! A defect in this metabolism results in the production of a substance in the body which is excreted in the sweat and the urine and smells like maple syrup. He could have diaphoresis where he sweat excessively all the time(the stink kind). If that is his worse symptom of whatever disease he has consider yourself lucky. Maple syrup urine disease can be classified by its pattern of signs and symptoms, or by its genetic cause. Despite the attempts of deodorant ads everywhere to convince us otherwise, people do not naturally smell like lilies and meadows. Like in humans, Canine Diabetes is a serious condition. Mundane Pointless Stuff I Must Share (MPSIMS) Stainz May 7, 2006, 5:45pm #1. Learn why urine may smell sweet, treatments, and when to see a doctor. People with this condition cannot break down the amino acids leucine, isoleucine, and valine. But anything is possible in this crazy world. Thiamine, also known as vitamin B1 plays an important part in protein metabolism. Dogsâ breath often smells funky, and a particularly bad stink can indicate serious illnesses like kidney disease and liver problems. Q: Why does my urine smell like maple syrup? If you notice that your sweat has begun to smell sweet, you should bring it to your doctor's attention. Classification. Today, doctors still recognize that some diseases, like yeast infections, carry distinctive odors. So, sometimes I wake up in the morning and my hands smell exactly like maple syrup. Maple syrup urine odor in children: Maple syrup urine odor in children is a child's urine that smells like maple syrup. So, before you start worrying about your blood sugar, rest assured that your odor is MOST LIKELY caused by your protein intake. Ive Googled my face off, and while I can find references to things like Maple Syrup Urine Disease or the sweet breath some diabetics get, I cant find anything on maple syrup â¦ Others claim that it smells like sweet cinnamon. So far our pediatrician is stumped, and all of his tests have been normal. He could have diaphoresis where he sweat excessively all the time(the stink kind). It would be wise to have your fasting blood glucose checked, especially if you have a family history of diabetes. (If you do, get yourself genetically sampled and market that sh*t.) We all sweat, and we all smell to varying degrees in response to our perspiration. My sweat smells like chocolate cake with a hint of coffee. These are the hallmarks of diabetes mellitus which can cause my patient to smell like maple syrup. Diagnosis of maple syrup urine disease. Be sure to tell your babyâs doctor that you're taking fenugreek. My Dogâs Breath Smells Like Maple Syrup. Pour some water down the drain, make sure it's not a gas coming up. Other than being a smart and goofy kiddo he's pretty regular. This involves pricking your baby's heel to collect drops of blood to test. Unusual body odors can range from fish to rotten eggs to maple syrup or apples. Maple syrup urine disease is a metabolic disorder that causes certain amino acids to â¦ He's not sick or unhealthy in any way that we can tell, and he hasn't been exposed to chemicals or drugs that we know of. I think it's her sweat that smells like it. The etiology of this is not known and it appears that in most cases it goes away on its own. My sweat smells like maple syrup!!! Charlie: Yeah. Causes. The urine of people with this condition can smell like maple syrup. Has anybody else experienced this with their babies? It is a genetic disorder, very unusual in occurrence. And I'm not kidding, either. My 7 year old son smells like gasoline and maple syrup when he sweats. Anonymous . And since it passes to the baby, it can also cause your babyâs urine and sweat to smell like maple syrup. I think I'm going to have to start taking that stuff. Poor feeding, vomiting, loss of appetite, irritability. The condition gets its name from the distinctive sweet odor of affected infants' urine, particularly prior to diagnosis and during times of acute illness. MSUD is considered an amino acid condition because people with MSUD have trouble breaking down certain amino acids, the building blocks of proteins. I donât know why something would smell like maple syrup in a house that is constructed like it is. See detailed information below for a list of 2 causes of Maple syrup urine odor in children, including diseases and drug side effect causes. Here is a video explaining this fenugreekâs side effect more: The problem with sotolon is that the body cannot digest it, so, it passes through the body relatively unchanged and thus making your sweat and your urine smell like maple syrup or concentrated curry spice. This may not always be present in all types. A: If you notice a very distinct sweet smell as you urinate, this could mean one of two things: maple syrup urine disease or diabetic ketoacidosis (DKA). I have never heard of someones sweat smelling like maple syrup. Tom: Right, but she said she checked the attic for bees. The disease is named so since; urine excreted by the baby or the child smells much like maple syrup. This leads to a buildup of these chemicals in the blood. The last 2 days my dd has smelt like maple syrup. Maple syrup urine disease (MSUD) is inherited, which means it is passed down through families. The substance responsible for the smell is sotolone (or 4,5-dimethyl-3-hydroxy-2[5H]-furanone for them sciency types), which is also present in the herbs lovage and fenugreek. It is caused by a defect in 1 of 3 genes. If that is his worse symptom of whatever disease he has consider yourself lucky. Same smell is pervading the Greenwich Village / NYU area -- â¦ Diabetes type 2 symptoms: High blood sugar signs include sweet-smelling breath (Image: GETTY Images) âDKA mainly affects people with type 1 diabetes, but â¦ October 28, 2005 02:38 AM. Ain't nothing wrong or weird about it. Maple syrup urine disease (MSUD) is a condition in which the body is unable to break down certain proteins. I seriously have a hint o' chocolate cake in my pits. 1 0. Absolutely, but as far as that goes, Iâd investigate the walls. Maple syrup urine odor in children: Introduction. Detecting MSUD early and beginning treatment can often â¦ But anything is possible in this crazy world. One of the characteristic symptoms of MSUD is sweet-smelling urine, which gives the condition its name. 0 0. The condition is named for the sweet odor of the urine of untreated babies. Tell us why. 1 decade ago. If he is taking a lot of whey protein powder, he's getting a lot of branched-chain amino acids, and they have an odor of maple syrup. December 14, 2015, 5:25pm #3. I would have your bf go get tested for Maple Syrup Urine disease....it â¦ However, there is a common condition that results in sweet breath: Canine Diabetes. Fenugreek will make your sweat smell like maple syrup, curry, burned sugar and tobacco, combined! At around 5 days old, babies are offered newborn blood spot screening to check if they have MSUD. Charlie: Well, itâs the bedroom-Tom: Those smell questions are tough. The most common form of maple syrup urine disease (MSUD) presents rapidly after birth and can be fatal if not treated. In any case, regardless of nuances, the sweet smell generally indicates that coolant is leaking somewhere in the vehicle's engine. The other cause of sweet smell in urine is an uncommon youth disease called maple sugar urine disease. 9 years ago. The whole city smells like maple syrup and everyone knows it! Urine, sweat, or earwax that smells like maple syrup or burnt sugar. Anonymous . (This disorder got its name from this common symptom.) A: There is a medical condition where children develop a maple syrup odor to their urine. Urine smell: Wee smelling like maple syrup could indicate a rare, inherited disorder Maple syrup urine disease (MSUD) is a condition where the body canât process certain amino acids. Smells and Medicine . Unless it hits high concentrations, which, with my new deodorant, never happens.